Arrhythmogenic right ventricular dysplasia (ARVD), refers to the primary forms of cardiomyopathy and is characterized by the replacement of the right ventricular (RV) myocardium with fibrous and adipose tissue with the development of life threatening arrhythmias. According to different authors, the prevalence of arrhythmogenic right ventricular dysplasia is 1 per 1000 population; other literature sources report that the incidence of ARVD is 1 per 5000 population. The ratio of the incidence of the disease among men and women in the population is 3:1. The nonspecificity of symptoms, clinical polymorphism, and the absence of a single method make the diagnosis of ARVD a difficult task.